文章摘要
叶丽,高灵素,丁美琪,等.特发性嗜酸粒细胞增多综合征 1例并文献复习[J].安徽医药,2020,24(8):1574-1576.
特发性嗜酸粒细胞增多综合征 1例并文献复习
Idiopathic hypereosinophilic syndrome: a case report and literature review
  
DOI:10.3969/j.issn.1009?6469.2020.08.024
中文关键词: 嗜酸粒细胞增多肌痛综合征  多系统损害  糖皮质激素  环磷酰胺
英文关键词: Eosinophilia?Myalgia syndrome  Multiple?system damage  Corticosteroid  Cyclophosphamide
基金项目:
作者单位
叶丽 六安市人民医院血液内科安徽六安 237005 
高灵素 六安市人民医院血液内科安徽六安 237005 
丁美琪 六安市人民医院血液内科安徽六安 237005 
虞国慧 六安市人民医院血液内科安徽六安 237005 
冯学艺 六安市人民医院 血管外科安徽六安 237005 
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中文摘要:
      目的提高对特发性嗜酸粒细胞增多综合征的认识。方法报告 2015年 10月 9日六安市人民医院收治的特发性嗜酸细胞增多综合征 1例,观察其临床表现及治疗经过,并进行文献复习。结果病人出现消化、神经、皮肤等多个系统损害,经激素治疗后好转,自行停药后,出现右侧肢体动静脉血栓,激素联合环磷酰胺治疗后病情改善。结论特发性嗜酸粒细胞增多综合征可以累及消化、神经、心血管、皮肤等多个系统,可以导致血栓形成等并发症,严重时可危及生命,早期诊断及治疗尤为重要。
英文摘要:
      Objective To improve the understanding of idiopathic hypereosinophilic syndrome(IHES).Methods A case of idio? pathic hypereosinophilic syndrome,who received treatment in The Lu’an People’s Hospital in October 9,2015,was selected.Its clinical manifestations and treatment were observed,and literature review was carried out.Results The patient developed damage to digestive system,nervous system and dermal system,which was improved after hormone therapy.After self?withdrawal of medica? tion,the patient developed arteriovenous thrombosis of the right limb,which was improved after hormone therapy combined with cy? clophosphamide.Conclusion Idiopathic hypereosinophilic syndrome can involve multiple systems,such as digestive,nervous,car? diovascular and dermal systems,and can lead to complications such as thrombosis.In severe cases,it can be life?threatening.Early diagnosis and treatment are especially important.
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