| 宋萌萌,谢媛媛,余炳前,等.额部纤维肉瘤型隆突性皮肤纤维肉瘤 1例[J].安徽医药,2023,27(7):1446-1448. |
| 额部纤维肉瘤型隆突性皮肤纤维肉瘤 1例 |
| A case of fibrosarcomatous dermatofibrosarcoma protuberans on forehead |
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| DOI：10.3969/j.issn.1009-6469.2023.07.038 |
| 中文关键词: 皮肤纤维肉瘤 波形蛋白 额部 胶原 Ⅰ型 皮脂腺肿瘤 病例报告 |
| 英文关键词: Dermatofibrosarcoma Vimentin Forehead Collagen type Ⅰ Sebaceous gland neoplasms Case reports |
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| 中文摘要: |
| 目的探讨纤维肉瘤型隆突性皮肤纤维肉瘤(fibrosarcomatous dermatofibrosarcoma protuberans，FS-DFSP)临床特点，以期提高对该病的认识，减少临床误诊。方法回顾性分析 2020年 7月兰州大学第二医院收治的 1例 FS-DFSP病人临床资料。结果病人因“额部肿块切除术后 10年，再发 1年”入院。皮损组织病理:短梭形细胞呈席纹状排列，部分区域呈束状、鱼骨样排列。免疫组化: CD34(+)、波形蛋白(Vimentin)(+)、Ki-67增生活跃区 60%(+)。诊断为 FS-DFSP，予以扩大范围皮肤病损根治性切除术，术后随访至今未见复发。结论 FS-DFSP发病率低，易误诊，提高对该病的认识及警惕性有助于确诊及降低临床误诊率。 |
| 英文摘要: |
| Objective To investigate the clinical characteristics of fibrosarcomatous dermatofibrosarcoma protuberans (FS-DFSP), in order to improve the understanding of the disease and reduce clinical misdiagnosis.Methods The clinical data of one patient diagnosed as FS-DFSP who admitted to Lanzhou University Second Hospital were retrospectively analyzed in July 2019.Results The patient was admitted to the hospital because a mass on his forehead that recieved excision procedure 10 years ago recurred for more thanone year. Histopathology of the skin lesions showed that short spindle cells were arranged in a mat pattern, and some areas were foundwith bundle-like and fishbone-like arrangement. Immunohistochemical staining showed that CD34 ( + ), Vimentin ( + ) and Ki-67 60% ( + ). Diagnosis of FS-DFSP was made and extensive radical resection of skin lesions was performed. No recurrence was found in postoperative follow-up up to now.Conclusion The incidence of FS-DFSP is low and it is easy to be misdiagnosed. To improve the awareness and vigilance of FS-DFSP is helpful to diagnose the disease and reduce the rate of clinical misdiagnosis. |
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